{"id":382,"date":"2021-04-04T11:20:24","date_gmt":"2021-04-04T11:20:24","guid":{"rendered":"https:\/\/drmehmettasdemir.com\/?p=382"},"modified":"2021-04-29T07:03:57","modified_gmt":"2021-04-29T07:03:57","slug":"bobreklerde-kist-varligi","status":"publish","type":"post","link":"https:\/\/drmehmettasdemir.com\/en\/bobreklerde-kist-varligi\/","title":{"rendered":"B\u00f6breklerde kist varl\u0131\u011f\u0131"},"content":{"rendered":"<p class=\"has-medium-font-size\">B\u00f6brekler v\u00fccuttan su ve toksik maddelerin uzakla\u015ft\u0131r\u0131lmas\u0131nda \u00f6nemli organlard\u0131r. B\u00f6brek i\u00e7inde kist varl\u0131\u011f\u0131 basit olabilece\u011fi gibi b\u00f6breklere ileri derecede zarar verebilecek \u015fekilde b\u00fcy\u00fcyebilir ve b\u00f6brek yetersizli\u011fine yol a\u00e7abilir.<\/p>\n\n\n\n<p class=\"has-medium-font-size\">B\u00f6brekte kistlerin var oldu\u011fu hastal\u0131klar g\u00f6receli olarak nadirdir ve \u00e7ocukluk \u00e7a\u011f\u0131nda \u00e7e\u015fitli formlarda saptanabilirler. Kistler izole olabilece\u011fi gibi bir sendromun par\u00e7as\u0131 da olabilirler. Her hal\u00fckarda b\u00f6brekte kist olan \u00e7ocuk (ve eri\u015fkinlerin) nefroloji uzman\u0131 taraf\u0131ndan d\u00fczenli izlemi gereklidir.<\/p>\n\n\n\n<hr class=\"wp-block-separator\"\/>\n\n\n\n<h3><strong>Kistler neden olu\u015fur?<\/strong><\/h3>\n\n\n\n<p class=\"has-medium-font-size\">Bebe\u011fin (fet\u00fcs\u00fcn) anne karn\u0131nda kal\u0131t\u0131msal olmayan geli\u015fim bozukluklar\u0131, genetik sorunlar ve nadiren de edinsel (sonradan geli\u015fen) nedenlere ba\u011fl\u0131 kistler olu\u015fabilir.<\/p>\n\n\n\n<h3>Hangi tip kistik b\u00f6brek hastal\u0131klar\u0131 var?<\/h3>\n\n\n\n<ol type=\"A\" class=\"has-medium-font-size\"><li><strong>Genetik Ge\u00e7i\u015fi Olmayan Kistik B\u00f6brek Hastal\u0131klar\u0131<\/strong><ul><li>\u0130zole b\u00f6brek kistleri: Basit ya da kompleks tip olabilir ve toplumda yayg\u0131n bulunur. Basit kistler \u00f6nemsizken kompleks kistler kanser geli\u015fimi a\u00e7\u0131s\u0131ndan izlenmelidir. Bu ayr\u0131m\u0131n doktor taraf\u0131ndan yap\u0131lmas\u0131 gereklidir.<\/li><li>Multikistik displastik b\u00f6brek: B\u00f6bre\u011fin anne karn\u0131nda geli\u015fim bozuklu\u011fu s\u00f6z konusudur. Genellikle tek b\u00f6brek etkilenir ve i\u00e7inde sa\u011fl\u0131kl\u0131 b\u00f6brek dokusu i\u00e7ermez. Erkeklerde daha s\u0131k olup sol taraf\u0131 daha \u00e7ok etkiler. Ya\u015fam\u0131n ilk 2-3. y\u0131l\u0131nda tutulan b\u00f6brekte bozulma belirginle\u015fir. Kar\u015f\u0131 b\u00f6bre\u011fin sa\u011fl\u0131kl\u0131 olmas\u0131 \u00e7ok \u00f6nemli ve izlenmesi gereken durumdur, bazen bu b\u00f6brekte de veziko\u00fcreteral refl\u00fc, hidronefroz gibi do\u011fu\u015ftan olabilen sorunlar olabilmektedir. Ayr\u0131ca b\u00f6brek d\u0131\u015f\u0131nda kalpte, yemek borusunda ve n\u00f6rolojik sistemde sorunlar a\u00e7\u0131s\u0131ndan de\u011ferlendirme yap\u0131lmal\u0131d\u0131r.<\/li><\/ul><\/li><li><strong>Genetik Ge\u00e7i\u015fi Olan Kistik B\u00f6brek Hastal\u0131klar\u0131<\/strong><ul><li><strong>Polikistik B\u00f6brek Hastal\u0131\u011f\u0131: <\/strong>Kal\u0131t\u0131msal (genetik ge\u00e7i\u015fli, ailesel) bir hastal\u0131kt\u0131r. Her iki b\u00f6brekte \u00e7ok say\u0131da kist varl\u0131\u011f\u0131 s\u00f6z konusudur ve iki tipi bulunur:<ul><li><strong>Otozomal dominant (bask\u0131n) polikistik b\u00f6brek hastal\u0131\u011f\u0131:<\/strong> En s\u0131k ailesel b\u00f6brek hastal\u0131\u011f\u0131d\u0131r, 400-1000 ki\u015fi de 1 g\u00f6r\u00fclmektedir. Etkilenen bireyin her \u00e7ocu\u011funa bu hastal\u0131\u011f\u0131 aktarma \u015fans\u0131 (\u015fanss\u0131zl\u0131\u011f\u0131 demek daha do\u011fru olur) %50\u2019dir. Etkilenen bireylerin \u00f6m\u00fcr boyu hi\u00e7 bulgusu olmayabilir ya da b\u00f6brek yetersizli\u011fi geli\u015febilir.<\/li><li><strong>Otozomal resesif (\u00e7ekinik) polikistik b\u00f6brek hastal\u0131\u011f\u0131: <\/strong>Daha nadirdir ve genellikle anne karn\u0131nda te\u015fhis edilir, daha az s\u0131kl\u0131kla ilerleyen \u00e7ocukluk d\u00f6neminde saptan\u0131r. S\u0131kl\u0131\u011f\u0131 yakla\u015f\u0131k 20 binde 1 olarak bildirilmektedir. Bu hastal\u0131kta iki ebeveynde de \u00e7ekinik halde genetik hastal\u0131k vard\u0131r ve kendilerini etkilememi\u015ftir. Bu ebeveynlerden olan her \u00e7ocu\u011fun hastal\u0131\u011fa sahip olma \u015fans\u0131z %25\u2019dir.<\/li><\/ul><\/li><\/ul><\/li><\/ol>\n\n\n\n<hr class=\"wp-block-separator\"\/>\n\n\n\n<h3>B\u00f6breklerde kistik hastal\u0131k varl\u0131\u011f\u0131 ne t\u00fcr sorunlara yol a\u00e7abilir?<\/h3>\n\n\n\n<p class=\"has-medium-font-size\">\u0130zole basit kistler genellikle herhangi bir soruna yol a\u00e7maz. Ancak \u00f6zellikle polikistik b\u00f6brek hastal\u0131klar\u0131nda <a href=\"https:\/\/drmehmettasdemir.com\/en\/cocuklarda-hipertansiyon-2\/\">hipertansiyon<\/a>, idrarda kan varl\u0131\u011f\u0131 (hemat\u00fcri), <a href=\"https:\/\/drmehmettasdemir.com\/en\/bobrek-taslari-2\/\">b\u00f6brek ta\u015flar\u0131<\/a>, <a href=\"https:\/\/drmehmettasdemir.com\/en\/bobregin-ve-idrar-yollarinin-dogumsal-sorunlari\/\">veziko\u00fcreteral refl\u00fc, hidronefroz<\/a> gibi do\u011fumsal di\u011fer anomaliler, kafa i\u00e7inde damar geni\u015flemeleri (anevrizma), karaci\u011fer kistleri veya fibrozis (karaci\u011fer yap\u0131s\u0131nda bozulma), kalp sorunlar\u0131 (\u00f6zellikle kalp kapaklar\u0131nda problemler) gibi sorunlar e\u015flik edebilmektedir. <\/p>\n\n\n\n<hr class=\"wp-block-separator\"\/>\n\n\n\n<h3>Tedavisi var m\u0131?<\/h3>\n\n\n\n<p class=\"has-medium-font-size\">Kistlerin b\u00fcy\u00fcmesini durdurmaya ve hatta k\u00fc\u00e7\u00fcltmeye y\u00f6nelik tedaviler eri\u015fkinlerde denenmektedir. Bu konuda umut veren geli\u015fmeler olsa da hen\u00fcz \u00e7ocukluk \u00e7a\u011f\u0131nda rahatl\u0131kla kullan\u0131labilecek ila\u00e7 tedavisi s\u00f6z konusu de\u011fildir. Bu hastal\u0131\u011f\u0131n y\u00f6netimi \u015fu \u015fekilde \u00f6zetlenebilir:<\/p>\n\n\n\n<ul class=\"has-medium-font-size\"><li>Kan bas\u0131nc\u0131 izlemi ve y\u00fcksek ise tedavisi \u00f6nemlidir.<\/li><li>Tuzdan k\u0131s\u0131tl\u0131 veya a\u015f\u0131r\u0131 tuz kayb\u0131 olan durumlarda yeterli destek ile beslenme gereklidir.<\/li><li>Protein k\u0131s\u0131tlanmas\u0131na gerek yoktur (b\u00f6brek yetersizli\u011fi olmad\u0131\u011f\u0131 s\u00fcrece).<\/li><li>\u0130drar yolu enfeksiyonu veya b\u00f6brek ta\u015flar\u0131 a\u00e7\u0131s\u0131ndan dikkatli izlem gereklidir.<\/li><li>B\u00f6brek yetersizli\u011fi geli\u015firse <a href=\"https:\/\/drmehmettasdemir.com\/en\/cocuk-bobrek-nakli\/\">b\u00f6brek nakli <\/a>ile \u00e7ok ba\u015far\u0131l\u0131 sonu\u00e7lar al\u0131nmaktad\u0131r.<\/li><li>\u00d6zellikle otozomal \u00e7ekinik tipte olan hastal\u0131kta b\u00f6brekler a\u015f\u0131r\u0131 b\u00fcy\u00fcyerek solunum s\u0131k\u0131nt\u0131s\u0131na yol a\u00e7abilir (kar\u0131n i\u00e7inde a\u015f\u0131r\u0131 yer kaplayarak akci\u011fere bas\u0131 yapabilir). Bu durumda b\u00f6breklerden en az\u0131ndan birinin al\u0131nmas\u0131 ve b\u00f6brek nakil haz\u0131rl\u0131klar\u0131 \u00f6nerilir. <\/li><\/ul>\n\n\n\n<p><\/p>","protected":false},"excerpt":{"rendered":"<p>B\u00f6brekler v\u00fccuttan su ve toksik maddelerin uzakla\u015ft\u0131r\u0131lmas\u0131nda \u00f6nemli organlard\u0131r. B\u00f6brek i\u00e7inde kist varl\u0131\u011f\u0131 basit olabilece\u011fi gibi b\u00f6breklere ileri derecede zarar verebilecek \u015fekilde b\u00fcy\u00fcyebilir ve b\u00f6brek yetersizli\u011fine yol a\u00e7abilir. B\u00f6brekte kistlerin var oldu\u011fu hastal\u0131klar g\u00f6receli olarak nadirdir ve \u00e7ocukluk \u00e7a\u011f\u0131nda \u00e7e\u015fitli formlarda saptanabilirler. Kistler izole olabilece\u011fi gibi bir sendromun par\u00e7as\u0131 da olabilirler. Her hal\u00fckarda b\u00f6brekte kist [&hellip;]<\/p>","protected":false},"author":1,"featured_media":440,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":[],"categories":[7],"tags":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v19.4 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>B\u00f6breklerde kist varl\u0131\u011f\u0131 - Prof. Dr. Mehmet Ta\u015fdemir<\/title>\n<meta name=\"description\" content=\"B\u00f6brekte kistlerin var oldu\u011fu hastal\u0131klar g\u00f6receli olarak nadirdir ve \u00e7ocukluk \u00e7a\u011f\u0131nda \u00e7e\u015fitli formlarda saptanabilirler. Kistler izole olabilece\u011fi gibi bir sendromun par\u00e7as\u0131 da olabilirler. Her hal\u00fckarda b\u00f6brekte kist olan \u00e7ocuk (ve eri\u015fkinlerin) nefroloji uzman\u0131 taraf\u0131ndan d\u00fczenli izlemi gereklidir.\" \/>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/drmehmettasdemir.com\/en\/bobreklerde-kist-varligi\/\" \/>\n<meta property=\"og:locale\" content=\"en_GB\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"B\u00f6breklerde kist varl\u0131\u011f\u0131\" \/>\n<meta property=\"og:description\" content=\"B\u00f6brekte kistlerin var oldu\u011fu hastal\u0131klar g\u00f6receli olarak nadirdir ve \u00e7ocukluk \u00e7a\u011f\u0131nda \u00e7e\u015fitli formlarda saptanabilirler. Kistler izole olabilece\u011fi gibi bir sendromun par\u00e7as\u0131 da olabilirler. Her hal\u00fckarda b\u00f6brekte kist olan \u00e7ocuk (ve eri\u015fkinlerin) nefroloji uzman\u0131 taraf\u0131ndan d\u00fczenli izlemi gereklidir.\" \/>\n<meta property=\"og:url\" content=\"https:\/\/drmehmettasdemir.com\/en\/bobreklerde-kist-varligi\/\" \/>\n<meta property=\"og:site_name\" content=\"Prof. Dr. Mehmet Ta\u015fdemir\" \/>\n<meta property=\"article:published_time\" content=\"2021-04-04T11:20:24+00:00\" \/>\n<meta property=\"article:modified_time\" content=\"2021-04-29T07:03:57+00:00\" \/>\n<meta property=\"og:image\" content=\"https:\/\/drmehmettasdemir.com\/wp-content\/uploads\/2021\/04\/kist.jpg\" \/>\n\t<meta property=\"og:image:width\" content=\"2048\" \/>\n\t<meta property=\"og:image:height\" content=\"1626\" \/>\n\t<meta property=\"og:image:type\" content=\"image\/jpeg\" \/>\n<meta name=\"author\" content=\"Mehmet Ta\u015fdemir\" \/>\n<meta name=\"twitter:card\" content=\"summary_large_image\" \/>\n<meta name=\"twitter:creator\" content=\"@drmtsdmr\" \/>\n<meta name=\"twitter:site\" content=\"@drmtsdmr\" \/>\n<meta name=\"twitter:label1\" content=\"Written by\" \/>\n\t<meta name=\"twitter:data1\" content=\"Mehmet Ta\u015fdemir\" \/>\n\t<meta name=\"twitter:label2\" content=\"Estimated reading time\" \/>\n\t<meta name=\"twitter:data2\" content=\"3 minutes\" \/>\n<script type=\"application\/ld+json\" class=\"yoast-schema-graph\">{\"@context\":\"https:\/\/schema.org\",\"@graph\":[{\"@type\":\"WebSite\",\"@id\":\"https:\/\/drmehmettasdemir.com\/#website\",\"url\":\"https:\/\/drmehmettasdemir.com\/\",\"name\":\"Prof. Dr. Mehmet Ta\u015fdemir\",\"description\":\"\u00c7ocuk Nefrolojisi - \u00c7ocuk Sa\u011fl\u0131\u011f\u0131 ve Hastal\u0131klar\u0131 (Pediatri)\",\"publisher\":{\"@id\":\"https:\/\/drmehmettasdemir.com\/#\/schema\/person\/15ea05f5e389d073c1e827e5d80522b2\"},\"potentialAction\":[{\"@type\":\"SearchAction\",\"target\":{\"@type\":\"EntryPoint\",\"urlTemplate\":\"https:\/\/drmehmettasdemir.com\/?s={search_term_string}\"},\"query-input\":\"required name=search_term_string\"}],\"inLanguage\":\"en-GB\"},{\"@type\":[\"WebPage\",\"MedicalWebPage\"],\"@id\":\"https:\/\/drmehmettasdemir.com\/bobreklerde-kist-varligi\/\",\"url\":\"https:\/\/drmehmettasdemir.com\/bobreklerde-kist-varligi\/\",\"name\":\"B\u00f6breklerde kist varl\u0131\u011f\u0131 - Prof. Dr. Mehmet Ta\u015fdemir\",\"isPartOf\":{\"@id\":\"https:\/\/drmehmettasdemir.com\/#website\"},\"datePublished\":\"2021-04-04T11:20:24+00:00\",\"dateModified\":\"2021-04-29T07:03:57+00:00\",\"description\":\"B\u00f6brekte kistlerin var oldu\u011fu hastal\u0131klar g\u00f6receli olarak nadirdir ve \u00e7ocukluk \u00e7a\u011f\u0131nda \u00e7e\u015fitli formlarda saptanabilirler. 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